Background and Objectives Ehlers-Danlos syndrome, an inherited connective tissue disease, is rarely seen in pregnancy. Presentation may be mild or severe, depending on which type of the syndrome the patient possesses.

Methods A 38-year-old woman with Ehlers-Danlos syndrome type II presented for cesarean delivery at 34 weeks' gestation with premature rupture of membranes and breech presentation.

Results A subarachnoid block was chosen to provide surgical anesthesia. No adverse side effects or complications developed.

Conclusion In patients with Ehlers-Danlos syndrome, it is important to be aware of which type is present and to be knowledgeable about and prepared for any potential complications.